Autosomal recessive distal renal tubular acidosis with secondary nephrogenic diabetes insipidus in newborn a case report

Renal tubular acidosis (RTA) with secondary nephrogenic diabetes insipidus is a rare disease in newborns. Renal tubular dysfunction should be considered as a differential diagnosis in babies who fail to thrive with dehydration, polyuria, hypokalemia and normal anionic gap metabolic acidosis. We present here a case of a term neonate with distal RTA and secondary nephrogenic diabetes insipidus who was successfully managed with intravenous fluids, potassium citrate and thiazide