RECURRENT EXTRA OSSEOUS EWING'S SARCOMA LEFT ARM - A CASE REPORT

Extraosseous Ewings Sarcoma is a rare malignant small round cell neoplasm of undifferentiated mesenchymal origin. Most commonly affects children and age group less than 20. Ewings sarcoma, Extraosseous Ewings saroma, Primitive neuro ectodermal tumour(PNET), Aesthesioblastoma, Askin tumour(PNET of chest wall) are all belongs to Ewings family of tumour (EFT). Less than hundred cases are reported all over the world. t(11 22)(q24 q12) translocation is common. A 27 year male presented with swelling in the left arm for past 6 months.1 year before excision biopsy done for swelling in the same region. MRI shows swelling in the subcutaneous plane, Biopsy shows EwingsPNET. CT chest normal. Wide local excision with latismus dorsi flap and split skin graft done followed by chemotherapy. Histopathology report came as small round cell with scanty cytoplasm and hyperchromatic nuclei with mitosis,CD 99 positivity suggestive of Ewings Sarcoma. On follow up for 1 year with no evidence of recurrence metastasis