SMALL BOWEL LEIOMYOMA IN A PATIENT WITH NEUROFIBROMATOSIS - A CASE REPORT AND REVIEW OF LITERATURE

Neurofibromatosis, an autosomal dominantly inherited disease occurs 1 in 3000 live births. The disease has varied manifestations in the skin, nervous tissue, bone and soft tissues. Gastrointestinal tract may also be involved with multiple Neurofibromas, giving rise to obscure gastrointestinal bleeding and obstruction. There is an increased association between benign small bowel Leiomyomas and Neurofibromatosis but this has been documented in very few instances. Due to its rarity, a high degree of suspicion for gastrointestinal tumor in patients with Neurofibromatosis is needed for timely diagnosis.Present report describes an interesting case of a small intestinal Leiomyoma in a patient with cutaneous Neurofibromatosis