Bilateral testicular tumor in a patient with adrenogenital syndrome: A conservative approach

Testicular tumors of the adrenogenital syndrome (TTAGS) are a rare disease, with a benign curse. We present the case of a 12-year-old patient with congenital adrenal hyperplasia (CAH), precocious puberty and bilateral testicular masses. Hormonal control had been adequate. Incidental finding of bilateral testicular masses, with negative testicular tumoral biomarkers. The patient underwent right testicular sparing surgery, finding an intraparenchymal nodular mass. Pathological study showed a TTAGS, positive for CD99, Melan A, inhibin and synaptophysin markers. Conservative management was decided.