Hypohidrotic ectodermal dysplasia – A case report

Ectodermal dysplasia is a hereditary disorder characterized by developmental dystrophies involving the ectodermal derivatives characterized by triad of signs comprising sparse hair, missing or abnormal teeth and inability to sweat. Ectodermal dysplasia may be divided into the Hypohidrotic form (x-linked recessive) and the Hydrotic form (Autosomal inherited).Here we present a case of a 34 years male with Hypohidrotic ectodermal dysplasia with partial anodontia of maxillary arch and complete anodontia of mandibular arch.