A Rare Antitiy Extrarenal Wilms Tumor: A Case Report

Introduction: Extrarenal Wilms tumor is extremely rare. The development of this tumor outside of the kidney parenchyma is rare. Case: 3 year old boy presented an abdominal pain. A mass was palpated anteriorly of the rectum on rectal examination. Magnetic Resonans (MR) scan with intravenous (IV) contrast revealed a 47x43x23 millimeters, heterogeneous pelvic mass located rectovesical area. At laparotomy, tumor was fixed at the level of anterior recto sigmoid joint. Pathologic diagnosis of the tumor was extrarenal Wilms tumor. There was no any leymphoid hypertrophy and metastasis. After complete tumor resection, tumor phase was accepted Stage 3 and chemotherapy and radiotherapy were administered according to the treatment protocol of the National Tumor Wilm's Study Group. A year after treatment, the patient has had no evidence of recurrence. Conclusion: It is important to include extrarenal Wilms tumor in the differential diagnosis of children with intrathoracic or retroperitoneal tumors. Because some of these tumors are located in the pelvis, they may be incorrectly diagnosed preoperatively as a pelvic teratoma or ovarian cysts.