Hypertrophic pachymeningitis IgG4 related, a rare presentation

Extraaxial pachymeningeal enhancement may arise from various benign or malignant processes, including transient postoperative changes, intracranial hypotension, neoplasms such as meningiomas, metastatic disease (from breast and prostate cancer), secondary CNS lymphoma, granulomatous disease or idiopathic.Hypertrophic pachymeningitis (HP) is an inflammatory condition in which the dura mater of the cranium or spine becomes thickened, leading to symptoms that result from mass effect, nerve compression, or vascular compromise.. Many times, no diagnosis is reached in such cases, the disease has been described as idiopathic HP. IgG4-related disease (IgG4-RD) is a recently described inflammatory condition known to cause tumefactive lesions at myriad anatomical locations.Here we present a case of IgG4 related pachymeningitis-a rare presentation