LONG QT SYNDROME. PART 2

Long QT syndrome (LQTS) is a potentially life-threatening canalopathy, accompanied by prolonged QT interval on a 12-channel ECG, syncopal conditions and a high risk for sudden cardiac death due to the development of torsade de pointes (TdP) polymorphic ventricular tachycardia. The primary goal in management of patients with LQTS at the present stage is prevention of undiagnosed forms, adequate treatment and prophylaxis, facilitated by the rapid development of molecular biology and genetics. The second part of the present review reflects the latest achievements in its diagnosis and management.