A rare case report of acinic cell carcinoma in 22 years old female patient

Acinic cell carcinoma (ACC) is a low-grade malignant salivary neoplasm. In the head and neck region, the parotid gland is the predominant site of origin and women are usually more frequently diagnosed than men. ACCs constitute approximately 6% to 8% of all salivary gland neoplasms, and 17% of primary salivary gland malignancies. ACC has a significant tendency to recur, to produce metastases (cervical lymph nodes and lungs), and may have an aggressive evolution. ACC can be misinterpreted because of its low grade histology, due to its benign appearance, encapsulated tumor, absence of necrosis and histologically similar to the normal parotid gland. Histopathologist should be aware and very vigilant while reporting this entity.