JUVENILE SYSTEMIC SCLEROSIS

Juvenile scleroderma encompasses a range of conditions unified by the presence of fibrosis in the skin. Juvenile scleroderma is divided into 2 major categories ,localized scleroderma (LS) which is largely limited to the skin , and systemic sclerosis (SSc) , with organ involvement. Juvenile scleroderma is a rare disease , with a prevalence of 1 in 1,00,000 of people. Localized scleroderma is far more common than systemic sclerosis in children. Auto immunity is the key process in the pathogenesis of both localized and systemic scleroderma . We report a rare case of Juvenile systemic sclerosis.