Primitive neuroectodermal tumor of the kidney with IVC thrombus and pulmonary metastases a case report

Primitive neuroectodermal tumor of the kidney is a rare pathological entity in urologic malignancies. Renal PNET occurs predominantly in young adults and has a tendency to be extremely aggressive. Here we present a case of a 32 year old lady who presented with hematuria and on evaluation was detected to have a renal mass with IVC thrombus and pulmonary metastases. She underwent a right open radical nephrectomy with vena caval thrombectomy.