Mayer Rokitansky Kuster Hauser (MRKH) syndrome -CASE REPORT

19 years old girl admitted with co not attained menarche. On examination secondary sexual characters are present appropriate to her age, general examination including height, blood pressure, CVS, RS, CNS, external genitalia normal. Blood investigations including thyroid profile, FSH, LH, prolactin, testosterone normal. Ultrasound, MRI showed hypo plastic uterus, normal ovaries. Karyotyping showed 46XX .Examination under anaesthesia revealed blind vagina of 2cm.on per rectal examination no distinct uterine structure felt. Diagnostic laparoscopy showed rudimentary uterine bud, bilateral normal ovaries. The patient was advised perineal dilation (Frank technique).