MULTICENTRIC PARAGANGLIOMA - A RARE CASE PRESENTATION

Multicentric paraganglioma are a rarest entity encountered in clinical practice. We report a rare case of carotid body tumor with metachronous tumor of the organ of zuckercandal. Our patient was operated 4 years back for carotid body tumor. Currently, the patient had complaints of headache, palpitations, sweating for past 1 year, blurring of vision for around 6 months and pain in right flank for 3 months. MRI and MIBG scan showed right infrarenal mass which was suggestive of a functional paraganglioma. Patient’s 24 hour urine metanephrine, nor metanephrine, and VMA were raised. It is well known that paragangliomas may be hereditary and may be a part of genetic syndromes. Appropriate genetic screening should be considered in patients and families when hereditary syndromes are suspected. Continued follow-up is necessary, however, as recurrence, metastasis and multicentric tumor may occur years later.