Retrobulbar haemorrhage in a Factor XIII deficiency patient a case report

Factor XIII deficiency is a rare bleeding disorder with an incidence of one in 2.5 million population. It presents with prolonged umbilical cord stump bleeding during neonatal period, delayed soft tissue bruising, mucosal bleeding and with life- threatening intra cranial haemorrhage. Here report a 14 years old boy, known case of factor XIII deficiency presented with acute proptosis and defective vision in the Right eye following Road Traffic Accident, diagnosed to have Retrobulbar haemorrhage, who was immediately underwent for hematoma evacuation with lateral canthotomy under general anesthesia and he received 6 units of cryoprecipitate before and after the procedure as per Hematologist instruction.Postoperatively, the retrobulbar hemorrhage regressed and vision improved to 6 6p