Rarest of the Rare: Esthesioneuroblastoma in a Young Male

Esthesioneuroblastoma is a rare tumor arising from the olfactory epithelium of the nasal vault which frequently invades the cranial base and orbit. Esthesioneuroblastoma has a bimodal age distribution between 11 and 20 years and between 51 and 60 years. Esthesioneuroblastoma accounts for approximately 1-5 % of intranasal cancers. Case reports published worldwide have been very few. Common presenting symptoms of Esthesioneuroblastoma include nasal obstruction, epistaxis, facial pain, diplopia, proptosis, and anosmia. Apart from being locally aggressive, it metastasizes widely by both hematogenous and lymphatic routes. The case is reported of a 22-year-old male patient with a Kadish stage C tumor with 3 months history of headache, nasal obstruction, anosmia, blurring of vision and epistaxis.