Solid Psudopapillary Neoplasm of the Pancreas in 11 Years Old Saudi Girl: Case Report and Review of Literature

Solid psudopapillary neoplasm (SPN) of the pancreas is a rare neoplastic entity representing around 0.13-2.7 % of pancreatic neoplasms [1]. In recent years, SPN has been reported more frequently and this might be attributed to increased awareness of this disease [2]. This entity was described in details in 1959 by Frantz but was first reported by Lichtenstein in 1933 [3, 4]. This neoplasm has been designated with many names through out years, until it was official recognized as a distinctive entity by the World Health Organization (WHO) in 1996 and was given the name SPN [1]. Information about SPN is mostly case reports and small case series. The first published case of SPN was by Frantz in 1959 when he described papillary cystic tumor of the pancreas, in a 2 years old male patient, who died while they attempted to perform pancreaticodoudenectomy on him [3]. In 1970, Hamoudi et al added an additional patient to the literature where they ultrastructure the features of the tumor with electron microscopy which in turn led to its acceptance of SPN as separate clinicopathological entity [5]. Since 1953, more than 700 cases of SPN were reported, the majority of them were reported in the last 10 years [7]. This can be attributed to increase of awareness of the tumor behavior and its clinicopathological features. Herein, we aim to summarize our experience with diagnosis and the surgical treatment of SPN in a female child, as we were suspecting the tumor radiologically and confirmed intra-operatively by cytology.