Vein of Galen Malformation- A Unique Congenital Malformation

Vein of Galen malformation (VGM) is a congenital arterio-venous fistula in the brain associated with cardiovascular and neurological complications leading to high morbidity and mortality. It may present from the newborn period to late childhood. We report a case of five month old male child who was admitted with increased head size since the age of one month, history of increased work of breathing since two days. Antifailure treatment was given. On correlating history, clinical examination, ultrasound of skull and two dimensional echo cardiography (2D-echo) the diagnosis of VGM with hydrocephalus with Atrial septal defect (ASD) with partial anomalous pulmonary venous drainage (PAPVD) was made. After stabilisation the child, embolisation was planned. This case deals with detection and management of VGM with hydrocephalus patient.