A Case of True Hermaphrodite Presenting as Cyclical Hematuria

True hermaphrodite (also known as ovotesticular disorder of sexual development or ovotesticular-DSD), is one of the rare varieties of disorder of sexual development. It is characterized by histologically confirmed both ovarian and testicular tissue in one individual. Here we report the case of a 16-year-old phenotypic male with 46, XX genotype (true hermaphrodite) presenting with cyclical hematuria and histologically diagnosed as ovotestis.