Anaesthetic Management of a Child with Klippel Feil Syndrome for Detethering of Spinal Cord: A Case Report

Klippel Feil syndrome is a type of bony disorder which is characterized by the abnormal fusion of two or more cervical vertebrae, which is usually present since birth. It is an autosomal dominant congenital defect. It is characterized by the classical triad of low posterior hairline, short webbed neck, restricted head and neck movements and mostly associated with a tuft of hair at lumbosacral region and torticollis (abnormal neck position). Many aspects of this syndrome are surfacing and is not clear whether it is a separate entity or if it is a part of congenital spinal deformities. Being anaesthesiologist we should be aware and ready to dealing with difficult airway management. Here we are reporting a case with same with anticipated airway difficulty and we managed the airway successfully with the help of video laryngoscope. We also kept ready fiberopetic bronchoscope as per standard institute protocol. We observed that video laryngoscope can be an alternative good option for dealing with such patients.