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LE SYNDROME DE LIMB BODY WALL COMPLEX A PROPOS DUN CAS ET REVUE DE LA LITTERATURE

Journal: International Journal of Advanced Research (Vol.10, No. 05)

Publication Date:

Authors : ; ;

Page : 869-873

Keywords : LBWC Syndrome Polymalformatif Laparoschisic Thoracoschisis Exencephalie Theories Diagnostic Antenatale;

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Abstract

Limb body wallcomplex (LBWC) is a rare poly malformative syndrome of unknownorigin, comprising major anomalies of the ventral body wall (thoracoabdominal) associatedwithother anomalies, includingthose of the limbsthatmay range frompositionaldeformity to agenesis, unusualcraniofacial malformations, and a variety of visceral anomalies thatinclude the heart, lungs, and genitourinary system. Twophenotypes are describeddepending on the feto-placentalattachment. We report a case of LBWC diagnosed post partum in a stillbornwith the following malformations: a large anterioromphalocele, spina bifida withmeningocele, and severescoliosis. The lowerlimbsappearedasymmetricalwithbilateral club feetassociatedwithpolydactyly. The stillbirthadheres to the placenta by a very short cord of 3 cm comprising 2 arteries and a vein.

Last modified: 2022-06-22 18:21:37