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UNE DYSPNEE AIGUE REVELATRICE DUN SYNDROME DE MOUNIER-KUHN : A PROPOS DUN CAS ET REVUE DE LITTERATURE

Journal: International Journal of Advanced Research (Vol.10, No. 07)

Publication Date:

Authors : ; ;

Page : 611-616

Keywords : Tracheobronchomegalia Mounier-Kuhn Syndrome Chest CT Diagnosis;

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Abstract

Mounier-Kuhn syndrome (MKS) is a rare entitycharacterised by an enlargedtrachea and main bronchi.Despite the century-long delaybetween the first description in 1932, itisstillunder-diagnosedwithonly 300 cases reported in the literature. Histologicallyitischaracterised by an atrophy of the smooth muscle and elastic fibres of the tracheobronchialtreeresulting in impairedmucociliary clearance. The respiratorysymptoms of MKS are non-specific and appear as a recurrentrespiratory infection. Chest CT remains the gold standard for diagnosistreatmentis non-specific and based on the control of associatedrespiratorydiseases, physiotherapy and sometimessurgery. We report here the case of a 61-year-old man with a history of chronicbronchitis and recurrentpneumonitiswhowasadmitted for acute dyspnea and in whom the diagnosis of MKSwasretained. A betterknowledge of the pathologywillallow an earlydiagnosis and prevention of complications. This case illustrates the latediagnosis and management.

Last modified: 2022-08-19 17:53:14