Diffuse Pulmonary Lymphangiomatosis : A Case Report and Review of the Literature |Biomedgrid

Cystic lymphangiomatosis is a benign malformative tumor of the lymphatic system most commonly affecting the cranio-facial, cervical or thoracic region, and usually found in childhood. Its abdominal and especially retro-peritoneal location is rarer. The clinical presentation is very polymorphic. The diagnosis is suggested by imaging, but it requires histological confirmation. Its treatment is surgical and not always easy.