Ormond’s Disease; Management Dilemma |Biomedgrid

Background: Retroperitoneal fibrosis (RPF) or Ormond's disease is a rare and extensive fibroinflammatory condition of unknown cause involving the abdominal aorta, iliac arteries, ureters and inferior vena cava with infiltration to the surrounding structure. Case Report: We report a case of an extensive benign retroperitoneal fibrosis (RPF) in a 62-year-old lady with the mass encasing abdominal aorta, common iliac, and inferior vena cava. There is a medialization and thickening of bilateral ureter causing obstructive uropathy. Patient was given a tapering dose of glucocorticoid treatment for three consecutive months. Percutaneous nephrostomy was constructed only for the left kidney. Repeated scan showed regression of the fibrosis with improvement of uropathy. The purpose of this case report is to highlight on the treatment approach of idiopathic RPF and to summarize the relevant literature.