AN UNUSUAL ASSOCIATION OF CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY: A CASE REPORT
Journal: International Journal of Advanced Research (Vol.13, No. 01)Publication Date: 2025-01-15
Authors : Mitra S. Biswas A.; Saha S.;
Page : 261-264
Keywords : Distal Acquired Demyelinating Symmetric Neuropathy (DADS) CIDP (Chronic Inflammatory Demyelinating Polyneuropathy) MGUS (Monoclonal Gammopathy of Undetermined Significance);
Abstract
Distal Acquired Demyelinating Polyneuropathy (DADS), a variant of Chronic Inflammatory Demyelinating Polyneuropathy (CIDP) is rarely associated with Monoclonal Gammopathy of Undetermined Significance. A case of quadriparesis is reported here, who was found to have DADS in background of MGUS IgA lambda. He was treated with intravenous Immunoglobulin and Azathioprine and showed good response. We report this case to sensitize the medical fraternity about the unusual association of CIDP with plasma cell dyscrasia.
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