Carcinoma ex Pleomorphic Adenoma (CXPA)-A rare parotid malignancy

Carcinoma ex pleomorphic adenoma (CXPA) is a rare parotid malignancy and its prognosis is poorer than other parotid malignancies. Invasive tumours tend to behave in a more aggressive fashion. These tumours are seen in patients in the sixth to seventh decades of their life. We present a 38-year-old male with a right-sided parotid gland swelling, which was present for the past 3 to 4 years and gradually increasing in size, with a solitary pulmonary nodule in the left upper lobe. On Fine Needle Aspiration Cytology (FNAC) of the parotid gland, a diagnosis of CXPA was given. This was confirmed by histopathology as CXPA with the malignant component of mucoepidermoid carcinoma and ductal carcinoma and with comedo pattern of necrosis.