A rare case of agenesis of dorsal pancreas

Dorsal pancreatic agenesis is an extremely rare congenital entity. Very few cases have been published in the literature about this congenital anomaly. Agenesis of the dorsal pancreas is associated with various anomalies, such as polysplenia syndrome, wandering spleen, interruption of the inferior vena cava, hemiazygos and azygos continuation, symmetrical liver, anomalous hepatic fissure or lobe, left-sided inferior vena cava, median gall bladder, inverted gallbladder and stomach, and intestinal malrotation. We have reported here an asymptomatic 31 year old male with incidental findings of hypoplasia of pancreatic body and absence of pancreatic tail on contrast enhanced abdominal computed tomography (CT) and similar findings were seen on Magnetic resonance imaging (MRI). Further Magnetic resonance cholangiopancreatography (MRCP) was done on which hypoplastic proximal MPD at body of pancreas with complete absent of MPD at tail region noted. The final diagnosis was dorsal pancreatic agenesis.