PLEXIFORM NEUROFIBROMATOSIS CASE REPORT

Introduction- Plexiform neurofibroma or Pachydermatocoele is an uncommon variety of generalized neurofibromatosis, usually associated with Trigeminal nerve. We report two cases of plexiformneurofibroma.case1)18 year girl with left forehead neurofibroma,case2) 14 year girl with right leg neurofibroma Clinical Presentation - The neurofibroma started in child hood. Family history of neurofibroma was positve in both the cases . Cafe' au lait spots,a useful diagnostic sign, seen in both patients. Intervention - Subtotal excision was done to correct cosmetic deformity. Conclusion -Surgical excision is the widely accepted form of treatment. Malignant changes to be ruled out by careful histopathological evaluation . Prognosis is usually good with early surgical treatment.