Bilateral Giant Angiomyolipoma in Tuberous Sclerosis

Neurocutaneous syndromes are rare disorders that result in lesions in both the central nervous system and skin. Tuberous sclerosis is an important neurocutaneous syndrome with urological implications ranging from benign cysts to renal cell carcinomas. Herein we report a 40 year old lady who presented with bilateral large renal masses with classical features of Tuberous Sclerosis.