RASMUSSEN ENCEPHALITIS - A CASE REPORT

Rasmussen Encephalitis is a rare, immune mediated disease characterized by refractory seizures, progressive neurological dysfunction and unilateral hemispheric atrophy. This disorder typically involves a single cerebral hemisphere, affecting mainly children and adolescents. We report a case of Rasmussen Encephalitis in a young girl who was admitted with complaints of recurrent focal motor seizures involving right upper and lower limbs for the past 5 years. There was a progressive increase in the seizure frequency and severity despite adequate drug compliance. Patient also developed progressive decline in the cognitive functions and speech disturbances with weakness of right upper and lower limbs for the past 2 years. Initial CT Brain done was normal. Periodic CT Brain imaging showed progressive atrophy of the entire left cerebral hemisphere.