STURGE - WEBER SYNDROME - A RARE CONGENITAL NEURODERMATOSIS - A CASE REPORT

We report an adult case of Sturge - Weber syndrome who presented with history ofseizures since childhood. He had all the classic clinical features of the syndrome and had alreadydeveloped the irreversible neurological and ocular complications of the syndrome. Computedtomography scan showed the tramline calcification so characteristic of the syndrome.Withanticonvulsants, the seizures were controlled and he showed clinical improvement. This caseunderscores the importance of early diagnosis of the syndrome and timely initiation of appropriate treatment before the disabling sequelae set in