MYOFIBROMATOSE INFANTILE: A PROPOS D UN CASINFANTILE MYO FIBROMATISIS : CASE REPORT

Introduction: Infantile myofibromatosis (IM) is a rare benign mesenchymal tumor. It performs various clinical aspects. This is the most common fibromatosis of the child; it is characterized by a proliferation of fibroblasts and myofibroblasts with particular perivascular disposition. Methods: We report a case of a male child presented with a cervical mass since birth. Clinical examination showed a well circumscribed mass in the right cervical region. The Tomography objectified a benign look mass embedded in the sterno-mastoid and surgical resection was decided. Results: The mass was resected at the age of 2 years and 4 months. Pathological examination with immunohistochemical study allows to retain the diagnosis of infantile myofibromatosis. Conclusion: IM is a rare tumor that shows clinicopathological characteristics well defined. It should be considered as a differential diagnosis in any child with a solitary or multiple mesenchymal tumor, particularly that occurring during the first two years of life. Through this observation pathological, clinical, etiopathogenic and cytogenetic characteristics of this infantile tumor are described.