Primary Synovial Sarcoma of the Kidney: An Unusual Presentation

The Synovial Sarcoma (SS) is a rare neoplasm, the fourth most common type of sarcoma. Most often located at the paraarticular region of inferior limbs and tendons. Renal presentation is more common among 15-40 years old patients with an average of 38 years. It predominates in the male gender, manifesting itself with a feeling of abdominal mass, hematuria and nonspecific signs. We report a 59-year-old female patient consults by pain in the right lumbar region plus emesis and hematuria, accompanied with a hard, painless palpable mass in the right upper quadrant. Computed Tomography (CT) scan revealed markedly enlarged right kidney, with heterogeneous density components. Right renal nephrectomy is performed. The pathology service concludes diagnosis of SS, which is favored by immunohistochemistry. Finally, the patient had a fatal outcome due to a recurrent tumor compromising the right renal fossa.