ADULT KAPOSIFORM HEMANGIOENDOTHELIOMA OF THE LEG COMPLICATED BY KASABAKH MERITT PHENOMENON

Kaposiform hemangioendothelioma is a rare, locally aggressive vascular neoplasm that mainly occurs during childhood . the tumor is often located on the skin but may be deeper. The development of KHE in adults is very rare, and its evolution towards KMP is exceptional. The KMP is defined as the combination of a deep thrombocytopenia and a vascular tumor, usually a KHE or a tuftted angioma. It is a life threatening pathology, because of the major risk of bleeding, and compression of vital structure. A multidisciplinary approach to treatment has to be employed.