DYSPLASTIC GANGLIOCYTOMA OF THE CEREBELLUM (LHERMITTE-DUCLOS SYNDROME) : A CASE REPORTJournal: International Journal of Advanced Research (Vol.8, No. 6)
Publication Date: 2020-07-17
Authors : B.Taibi O. Ayouche Fz. Lamrani; L. Jroundi;
Page : 1506-1509
Keywords : International Journal of Advanced Research (IJAR);
Lhermitte-Duclos disease or dysplastic cerebellar gangliocytoma is a rare entity characterized by a hamartomatous lesion in the posterior fossa. Cowden's syndrome or hamartoma-neoplasia syndrome is a rare underdiagnosed autosomal dominant genodermatosis with a high incidence of malignant tumors. We report the case of a 42-year-old man presented with a cerebellar syndrome, Magnetic resonance (MR) imaging of the brain was performed and revealed a cerebellar left lesion suggestive of a Lhermitte-Duclos disease. At operation, a demarcated lesion was excised from the apparently normal surrounding cerebellar tissue and proved histologically to be Lhermitte-Duclos disease.
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