Cantrell Pentalogy-Arare Congenital Disorder

Cantrell pentalogy is a rare congenital thoraco-abdominal disruption with five characteristic Ectopia cordis and intracardiac anomalies, lower sternal defect, Midline supraumbilical thoraco-abdominal wall defect, anterior diaphragmatic defect, defect of diaphragmatic part of pericardium that results in relation between pericardial cavity and peritoneum. A diagnosis of pentalogy of Cantrell can often be made prenatally using a fetal ultrasound. Detail evaluation requires CT scan with contrast study. Long term prognosis is poor even in super speciality hospital and even after multiple corrective surgeries, morbity and mortalities are high.