A Rare Case of Ameloblastic Carcinoma involving the Ethmoid and Sphenoidal Sinus

Ameloblastic Carcinoma is an extremely rare malignant epithelial odontogenic tumour about which there is very little in literature. It is an aggressive neoplasm that is locally invasive and can spread to regional lymph nodes and also to distant sites such as lungs and bones. Histopathology plays a vital role in diagnosing Ameloblastic Carcinoma and differentiating it from Ameloblastoma. Here we present a unique case of Ameloblastic Carcinoma involving the ethmoidal and sphenoidal sinus in a 30 year old female patient which presented a diagnostic challenge. The patient was treated successfully with wide local excision followed by chemo radiation. Given the rarity of the disease and location this report constitutes a valuable contribution to current literature.