GIANT CONGENITAL NEVUS WITH PLEXIFORM NEUROFIBROMA AND EPITHELOID VARIANT OF MALIGNANT PERIPHERAL NERVE SHEATH TUMOR WITH MELANOCYTIC DIFFERENTIATION A RARE CASE REPORT

A 22 year male patient with a giant congenital nevus in association with plexiform neurofibroma and epitheloid malignant peripheral nerve sheath tumor (MPNST) on the trunk and back. This is a very rare entity, till now only two cases has been reported in the literature. The clinical, surgical and histological aspects of the disease are discussed. The mutual origin of all the three entities can be explained by boland theory of neurochristopathy.