MELANOTIC NEUROECTODERMAL TUMOR OF INFANCY IN 4 MONTHS OLD GIRL, A RARE CASE REPORT

Melanotic neuroectodermal tumour of infancy (MNTI) is an uncommon pigmented neoplasm of neural crest origin. A 4 months old female child presented with swelling at the upper gum , size measuring 2.5cm x 2.5 cm x2.0 cm. . USG and MRI suggestive of low grade lytic lesion- ? Congenital granular cell myeloblastoma/ ? Other lytic bony lesion /?congenital epulis of newborn. Microscopic examination showed dual population of cells , small round blue cells with hyperchromatic nuclei and scant cytoplasm in nodular arrangement surrounded by brown pigment containing epithelial cells and dense fibrosis with areas of ossification in the background. IHC showed positivity for HMB-45,NSE and synaptophysin .The final diagnosis was made as Melanotic neuroectodermal tumour of infancy (MNTI).