Primary Pulmonary Fibrosarcoma with Bone Metastasis: A Rare Case Report

Introduction: Fibrosarcomaia a rare and high level tumor that were derived from mesenchymal cell, arises from pulmonary parenchyma, the pulmonary artery, its branches, and the bronchi. The prevalence of primary pulmonary sarcomas are extremely rare, only 0.1 to 0.5% from all of pulmonary neoplasm cases. The undifferentiated pleomorphic sarcoma (UPS) is a rare tumor, which found for less than 0.2% of all lung tumor cases. Case: This is a case report of rare Primary pulmonary Fibrosarcoma with bone metastases by discovering apositive vimentinstaining indicates the mesenchymal origin of fibrosarcoma. However, the family of patient refused treatment. Conclusion: Radical resection is considered to be the only treatment that can achieve cure or prolong survival if the tumor appears to be resectable. Chemotherapy in patients with advanced - phase fibrosarcomas is based on anthracyclines as the first - line treatment, and doxorubicin is the most commonly used drug.