Orbital Rhabdomyosarcoma: Current Perspectives

Orbital rhabdomyosarcoma is mesenchymal tumor, presents 10-20% of all rhabdomyosarcoma are usually diagnosed in children. It presents clinically by rapidly progressive unilateral proptosis. Imaging is fundamental to assessing the extent of the tumor and the erosion of the bone, but only histology can confirm the diagnosis. The treatment involves a combination of chemotherapy, radiotherapy and surgery. The challenge is to choose a treatment with good cosmetic and functional results specially visual function and excellent survival.