Unascended Left Kidney with Malrotation: A Rare Congenital Anomaly

Anomalies of kidney form a significant portion of congenital malformations. Anomalies may occur in the number, position, shape, size and rotation of kidney. Structural, positional and vascular anomalies are the most frequently reported. Rotational anomalies form a rare entity not cited in most of the embryology textbooks. We present a case of unilateral unascended left kidney with malrotation in a male cadaver which was associated with other visceral and vascular variations. An attempt has been made to systematically document these variations and give possible explanations for the same. A detailed knowledge of these morphological variations will be useful for many urological and radiological procedures.