SPINAL EXTRADURAL PRIMITIVE NEUROECTODERMAL TUMOUR IN A CHILD A CASE REPORT

Primary spinal cord extradural primitive neurectodermal tumors are rare . These belong to a category of aggressive childhood malignancies . They pose a significant challenge in the management . Primary spinal extradural PNET most commonly occur in children and young adults . So far around fifty cases have been reported in the literature . This case is presented for its rarity and also for its typical presentation . These tumors are highly aggressive and have a rapid growth . This 6 year female child underwent gross total excision of the extradural tumor . Review of the literature shows that the overall prognosis is very poor even with surgery , chemotherapy and radiotherapy .