A RARE PRESENTATION OF ANCA ASSOCIATED VASCULITIS

Churg Strauss Syndrome (CSS) is a rare antineutrophil cytoplasmic antibody (ANCA associated small vessel vasculitis with protean manifestations. A 27 years old male presented with ulcer over legs, peripheral gangrene, mononeuritis multiplex, blood eosinophilia, pANCA negativity, later developed bronchial asthma, diffuse nodular pulmonary infiltrates, pANCA positivity, granuloma and renal failure inspite of treatment. In conclusion vasculitic manifestations are protean. It may have typical and atypical presentations. Repeated clinical examination and investigations will clinch the correct diagnosis as well as its complications, relapse and treatment failure.