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A case report - Congenital Cutaneous Kaposiform haemangioendothelioma

Journal: University Journal of Pre and Paraclinical Sciences (Vol.2, No. 3)

Publication Date:

Authors : ;

Page : 92-95

Keywords : Kaposiform haemangioendothelioma(KHE); Kasabach- Merritt syndrome(KMS); Thrombocytopenia.;

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Kaposiform haemangioendothelioma is a rare, locally aggressive vascular lesion ofinfancy and childhood, often associated with Kasabach- Merritt syndrome and lymphangiomatosis(1,2).Despite the rarity of this lesion, the morphological and clinical appearancesdistinguish it from other mimics(2,3) . As congenital form of haemangioendothelioma is very rare (3), it preluded the reporting of this case. This case is a male infant born with a large violaceous patch over the right loin extending to the back measuring about 12x8cm. No similar or deep lesions were found elsewhere. Incisional biopsy revealed the diagnosis of Kaposiform haemangioendothelioma. The tumor was immunoreactive to CD31 and CD34. A late onset of Kasabach- Merritt syndrome was noted.

Last modified: 2016-08-23 15:55:28