QUADRICUSPID AORTIC VALVE WITH ABERRANT CORONARY OSTIA - A CASE REPORT

Quadricuspid aortic valve is an uncommon congenital cardiac anomaly often detected incidentally or in association with other congenital cardiac anomaly. The incidence is about 0.003 percent in autopsy studies (1). They may also be associated with coronary anomalies, septal defects, patent ductus arteriosus, mitral or pulmonary valve malformations and conduction defects (2).If undetected in childhood, they may progress to aortic valvular dysfunction later in life, necessitating valve replacement. Associated coronary anomalies, if any, may make prosthetic replacement of the valve challenging. We herein describe a case of a quadricuspid aortic valve who presented with severe aortic regurgitation. She was detected to have low lying right coronary ostia, necessitating precautions during valve replacement.