A case of Hemi-Convulsions- HHE Syndrome

Hemiconvulsion-Hemiplegia-epilepsy syndrome (HHE) is focal epilepsy, a rare epileptic syndrome characterized by prolonged partial epilepsy producing hemiplegia sometimes followed by epilepsy disorder(1). We report 19 yr male with right hemiplegia, history of prolonged unilateral seizures since 4yrs of age, with evidence of left hemispheric atrophy on magnetic resonance imaging (MRI).The pathogenesis of HHE syndrome is likely to be due to histotoxic epileptic brain damage following prolonged focal convulsion due to any cerebral insult (2). Here we present a case of Idiopathic HHE syndrome related to poorly treated febrile seizures in childhood. Keyword :Hemi-convulsions