A CASE OF JUVENILE DERMATOMYOSITIS WITH PERITONEAL CALCIFICATION

Juvenile Dermatomyositis is a multisystem disease characterized by acute and chronic nonsuppurative inflammation of skin and striated muscle. Calcinosis is one of the hallmark squeal of juvenile dermatomyositis, and despite recent progress in the therapy of these disorders, dystrophic calcification still occurs in approximately one-third of patients. Ectopic calcification in JDM is thought to develop through a dystrophic mechanism. The sites most frequently affected are the elbows, knees, digits and extremities, although it may occur virtually anywhere over the body. This complication can cause significant debility with severe pain, skin ulceration, muscle atrophy, joint contracture, and acro osteolysis. Although various clinical patterns of calcification have been described peritoneal calcification is not reported so far. We report a case of Juvenile Dermatomyositis with extensive visceral peritoneal calcification.