Esthesioneuroblastoma presenting with proptosis and cervical lymphadenopathy - An unusual presentation

IntroductionEsthesioneuroblastoma is a rare tumor arising from the olfactory epithelium of the nasal vault which frequently invades the cranial base, cranial vault and orbit. Esthesioneuroblastoma (ENB) presenting simultaneously with proptosis and cervical lymph node metastasis is a very rare presentation.This case report is to discuss the radiation outcome of a patient with Esthesioneuroblastoma, with proptosis and neck metastasis, presented to our Department. Case Report Twenty six year old female presented with proptosis and loss of vision right eye and enlarged cervical lymph nodes for a period of two months whose MRI showed mass in the nasal cavity extending to right maxilla, ethmoid and orbit. HPE showed Esthesioneuroblastoma. Since surgery not possible, the patient was treated with chemo radiotherapy. The tumour completely responded to chemo radiation and proptosis relieved. The cervical lymph nodes also disappeared completely. The purpose of this study is to report the good radiation outcome of this rare nasal tumour with rare presentation