UNDIFFERENTIATED (EMBRYONAL) SARCOMA OF THE LIVERA CASE REPORT

Abstract : Primary hepatic tumors are rare, but unfortunately two-thirds of them are malignant, representing the third most common abdominal cancer encountered in paediatric practice, after Wilms tumor and neuroblastoma (1). Undifferentiated (embryonal) sarcoma of liver, which has also been termed mesenchymal sarcoma, malignant mesenchymoma, primary sarcoma of the liver and fibromyxosarcoma is uncommon and typically occurs during the first two decades of life. It is probably the third most common primary malignant hepatic tumour of children, after hepatoblastoma and hepatocellular carcinoma (2). The typical presentation is that of an abdominal mass and pain but fever is a variable feature. The treatment for the embryonal sarcoma of the liver is surgical resection, with adjuvant chemotherapy and possibly radiation therapy. The prognosis is generally poor.