Malignant Peripheral Nerve Sheath Tumour In Von Recklinghausens disease a rare case report

Malignant peripheral nerve sheath tumors (MPNSTs) are rare soft tissue tumors that arise from a peripheral nerve or exhibit nerve sheath differentiation. Most of these tumors arise from trunk, extremities, or head and neck regions. They are very rarely located in the abdominal cavity. We report a rare case of MPNST which presented as mass abdomen.